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Variation in amount of wild-type transthyretin in different fibril and tissue types in ATTR amyloidosis
Familial transthyretin (TTR) amyloidosis is caused by a mutation in the TTR gene, although wild-type (wt) TTR is also incorporated into the amyloid fibrils. Liver transplantation (LT) is the prevailing treatment of the disease and is performed in order to eliminate the mutant TTR from plasma. The ou...
Autores principales: | Ihse, Elisabet, Suhr, Ole B., Hellman, Ulf, Westermark, Per |
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Formato: | Texto |
Lenguaje: | English |
Publicado: |
Springer-Verlag
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3022153/ https://www.ncbi.nlm.nih.gov/pubmed/21107516 http://dx.doi.org/10.1007/s00109-010-0695-1 |
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