Accumulation of lysosulfatide in the brain of arylsulfatase A-deficient mice

Lysosomal storage diseases are a group of disorders where accumulation of catabolites is manifested in the lysosomes of different cell types. In metachromatic leukodystrophy (Arylsulfatase A [EC.3.1.6.8] deficiency) storage of the glycosphingolipid sulfatide in the brain leads to demyelination, resu...

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Detalles Bibliográficos
Autores principales: Blomqvist, Maria, Gieselmann, Volkmar, Månsson, Jan-Eric
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Short Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3041674/
https://www.ncbi.nlm.nih.gov/pubmed/21299873
http://dx.doi.org/10.1186/1476-511X-10-28

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3041674/
https://www.ncbi.nlm.nih.gov/pubmed/21299873
http://dx.doi.org/10.1186/1476-511X-10-28

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