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Accumulation of lysosulfatide in the brain of arylsulfatase A-deficient mice
Lysosomal storage diseases are a group of disorders where accumulation of catabolites is manifested in the lysosomes of different cell types. In metachromatic leukodystrophy (Arylsulfatase A [EC.3.1.6.8] deficiency) storage of the glycosphingolipid sulfatide in the brain leads to demyelination, resu...
| Autores principales: | , , |
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| Formato: | Texto |
| Lenguaje: | English |
| Publicado: |
BioMed Central
2011
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| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3041674/ https://www.ncbi.nlm.nih.gov/pubmed/21299873 http://dx.doi.org/10.1186/1476-511X-10-28 |