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Fatigue-inducing stimulation resolves myotonia in a drug-induced model

BACKGROUND: Slowed muscle relaxation is the contractile hallmark of myotonia congenita, a disease caused by genetic CLC-1 chloride channel deficiency, which improves with antecedent brief contractions ("warm-up phenomenon"). It is unclear to what extent the myotonia continues to dissipate...

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Detalles Bibliográficos
Autores principales: van Lunteren, Erik, Spiegler, Sarah E, Moyer, Michelle
Formato: Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3052176/
https://www.ncbi.nlm.nih.gov/pubmed/21356096
http://dx.doi.org/10.1186/1472-6793-11-5