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Isolated adult hypoganglionosis presenting as sigmoid volvulus: a case report

INTRODUCTION: Isolated hypoganglionosis is a rare cause of intestinal innervation defects. It is characterized by sparse and small myenteric ganglia, absent or low acetylcholinesterase activity in the lamina propria and hypertrophy of the muscularis mucosae, principally in the region of the colon an...

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Detalles Bibliográficos
Autores principales: Qadir, Irfan, Salick, Muhammad Musa, Barakzai, Abrar, Zafar, Hasnain
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3179760/
https://www.ncbi.nlm.nih.gov/pubmed/21902826
http://dx.doi.org/10.1186/1752-1947-5-445