Type IV Ehlers-Danlos Syndrome: A Surgical Emergency? A Case of Massive Retroperitoneal Hemorrhage

Retroperitoneal hemorrhagic bleeding is a known manifestation of Type-IV Ehlers-Danlos Syndrome that is caused by loss-of-function mutations of the pro-alpha-1 chains of type III pro-collagen (COL3A1) resulting in vascular fragility. A number of previous reports describe futile surgical intervention...

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Detalles Bibliográficos
Autores principales: Chun, Stephen G, Pedro, Patrick, Yu, Mihae, Takanishi, Danny M
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Bentham Open 2011
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3182407/
https://www.ncbi.nlm.nih.gov/pubmed/21966332
http://dx.doi.org/10.2174/1874192401105010210

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3182407/
https://www.ncbi.nlm.nih.gov/pubmed/21966332
http://dx.doi.org/10.2174/1874192401105010210

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