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Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway
Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation.
| Autores principales: | , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
Springer Netherlands
2010
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3249182/ https://www.ncbi.nlm.nih.gov/pubmed/21104317 http://dx.doi.org/10.1007/s10545-010-9236-x |