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Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway
Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation.
| Autores principales: | , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
Springer Netherlands
2010
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| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3249182/ https://www.ncbi.nlm.nih.gov/pubmed/21104317 http://dx.doi.org/10.1007/s10545-010-9236-x |
| _version_ | 1782220305332174848 |
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| author | Wanders, Ronald J. A. Duran, Marinus Loupatty, Ference J. |
| author_facet | Wanders, Ronald J. A. Duran, Marinus Loupatty, Ference J. |
| author_sort | Wanders, Ronald J. A. |
| collection | PubMed |
| description | Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation. |
| format | Online Article Text |
| id | pubmed-3249182 |
| institution | National Center for Biotechnology Information |
| language | English |
| publishDate | 2010 |
| publisher | Springer Netherlands |
| record_format | MEDLINE/PubMed |
| spelling | pubmed-32491822012-01-11 Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway Wanders, Ronald J. A. Duran, Marinus Loupatty, Ference J. J Inherit Metab Dis Branched-Chain Amino Acids Valine is one of the three branched-chain amino acids which undergoes oxidation within mitochondria. In this paper, we describe the current state of knowledge with respect to the enzymology of the valine oxidation pathway and the different disorders affecting oxidation. Springer Netherlands 2010-11-23 2012 /pmc/articles/PMC3249182/ /pubmed/21104317 http://dx.doi.org/10.1007/s10545-010-9236-x Text en © The Author(s) 2010 https://creativecommons.org/licenses/by-nc/4.0/ This article is distributed under the terms of the Creative Commons Attribution Noncommercial License which permits any noncommercial use, distribution, and reproduction in any medium, provided the original author(s) and source are credited. |
| spellingShingle | Branched-Chain Amino Acids Wanders, Ronald J. A. Duran, Marinus Loupatty, Ference J. Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title | Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title_full | Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title_fullStr | Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title_full_unstemmed | Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title_short | Enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| title_sort | enzymology of the branched-chain amino acid oxidation disorders: the valine pathway |
| topic | Branched-Chain Amino Acids |
| url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3249182/ https://www.ncbi.nlm.nih.gov/pubmed/21104317 http://dx.doi.org/10.1007/s10545-010-9236-x |
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