Dystrophin deficiency exacerbates skeletal muscle pathology in dysferlin-null mice

BACKGROUND: Mutations in the genes coding for either dystrophin or dysferlin cause distinct forms of muscular dystrophy. Dystrophin links the cytoskeleton to the sarcolemma through direct interaction with β-dystroglycan. This link extends to the extracellular matrix by β-dystroglycan's interact...

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Detalles Bibliográficos
Autores principales: Han, Renzhi, Rader, Erik P, Levy, Jennifer R, Bansal, Dimple, Campbell, Kevin P
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2011
Materias:
Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3287108/
https://www.ncbi.nlm.nih.gov/pubmed/22132688
http://dx.doi.org/10.1186/2044-5040-1-35

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3287108/
https://www.ncbi.nlm.nih.gov/pubmed/22132688
http://dx.doi.org/10.1186/2044-5040-1-35

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