Distinct Effects of Contraction-Induced Injury In Vivo on Four Different Murine Models of Dysferlinopathy

Mutations in the DYSF gene, encoding dysferlin, cause muscular dystrophies in man. We compared 4 dysferlinopathic mouse strains: SJL/J and B10.SJL-Dysf(im)/AwaJ (B10.SJL), and A/J and B6.A-Dysf(prmd)/GeneJ (B6.A/J). The former but not the latter two are overtly myopathic and weaker at 3 months of ag...

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Detalles Bibliográficos
Autores principales: Roche, Joseph A., Ru, Lisa W., Bloch, Robert J.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2012
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3303924/
https://www.ncbi.nlm.nih.gov/pubmed/22431915
http://dx.doi.org/10.1155/2012/134031

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3303924/
https://www.ncbi.nlm.nih.gov/pubmed/22431915
http://dx.doi.org/10.1155/2012/134031

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