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Familial Hypobetalipoproteinemia-Induced Nonalcoholic Steatohepatitis

Familial hypobetalipoproteinemia (FHBL) is a rare genetic disorder of lipid metabolism that is associated with abnormally low serum levels of low-density lipoprotein (LDL) cholesterol and apolipoprotein B. It is an autosomal co-dominant disorder, and depending on zygosity, the clinical manifestation...

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Detalles Bibliográficos
Autores principales: Lam, Mindy C.W., Singham, Janakie, Hegele, Robert A., Riazy, Maziar, Hiob, Matti A., Francis, Gordon, Steinbrecher, Urs P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3398101/
https://www.ncbi.nlm.nih.gov/pubmed/22855658
http://dx.doi.org/10.1159/000339761