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Familial Hypobetalipoproteinemia-Induced Nonalcoholic Steatohepatitis
Familial hypobetalipoproteinemia (FHBL) is a rare genetic disorder of lipid metabolism that is associated with abnormally low serum levels of low-density lipoprotein (LDL) cholesterol and apolipoprotein B. It is an autosomal co-dominant disorder, and depending on zygosity, the clinical manifestation...
Autores principales: | Lam, Mindy C.W., Singham, Janakie, Hegele, Robert A., Riazy, Maziar, Hiob, Matti A., Francis, Gordon, Steinbrecher, Urs P. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
S. Karger AG
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3398101/ https://www.ncbi.nlm.nih.gov/pubmed/22855658 http://dx.doi.org/10.1159/000339761 |
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