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Role of Prion Protein Aggregation in Neurotoxicity

In several neurodegenerative diseases, such as Parkinson, Alzheimer’s, Huntington, and prion diseases, the deposition of aggregated misfolded proteins is believed to be responsible for the neurotoxicity that characterizes these diseases. Prion protein (PrP), the protein responsible of prion diseases...

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Detalles Bibliográficos
Autores principales: Corsaro, Alessandro, Thellung, Stefano, Villa, Valentina, Nizzari, Mario, Florio, Tullio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Molecular Diversity Preservation International (MDPI) 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3430257/
https://www.ncbi.nlm.nih.gov/pubmed/22942726
http://dx.doi.org/10.3390/ijms13078648