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Tissue-Specific Strategies of the Very-Long Chain Acyl-CoA Dehydrogenase-Deficient (VLCAD(−/−)) Mouse to Compensate a Defective Fatty Acid β-Oxidation
Very long-chain acyl-CoA dehydrogenase (VLCAD)-deficiency is the most common long-chain fatty acid oxidation disorder presenting with heterogeneous phenotypes. Similar to many patients with VLCADD, VLCAD-deficient mice (VLCAD(−/−)) remain asymptomatic over a long period of time. In order to identify...
Autores principales: | Tucci, Sara, Herebian, Diran, Sturm, Marga, Seibt, Annette, Spiekerkoetter, Ute |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2012
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3443214/ https://www.ncbi.nlm.nih.gov/pubmed/23024820 http://dx.doi.org/10.1371/journal.pone.0045429 |
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