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86 The Efficacy and Safety of Human Plasma-derived C1-Inhibitor Concentrate Administered for the Treatment of Attacks in Pediatric Patients with Hereditary Angioedema Due to C1-Inhibitor Deficiency

BACKGROUND: Hereditary angioedema due to C1-inhibitor deficiency (HAE-C1-INH) is a life-threatening, rare disease characterized by recurrent edematous attacks. In 50% of cases, the initial onset of symptoms occurs between 5 and 11 years of age. There are limited data on the emergency treatment of ac...

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Detalles Bibliográficos
Autores principales: Farkas, Henriette, Csuka, Dorottya, Zotter, Zsuzsanna, Szabó, Erika, Kelemen, Zsuzsanna, Varga, Lilian, Fejes, János, Harmat, George
Formato: Online Artículo Texto
Lenguaje:English
Publicado: World Allergy Organization Journal 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3513084/
http://dx.doi.org/10.1097/01.WOX.0000411831.77376.a6