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Rimmed Vacuoles in Becker Muscular Dystrophy Have Similar Features with Inclusion Myopathies

Rimmed vacuoles in myofibers are thought to be due to the accumulation of autophagic vacuoles, and can be characteristic in certain myopathies with protein inclusions in myofibers. In this study, we performed a detailed clinical, molecular, and pathological characterization of Becker muscular dystro...

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Detalles Bibliográficos
Autores principales: Momma, Kazunari, Noguchi, Satoru, Malicdan, May Christine V., Hayashi, Yukiko K., Minami, Narihiro, Kamakura, Keiko, Nonaka, Ikuya, Nishino, Ichizo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3522649/
https://www.ncbi.nlm.nih.gov/pubmed/23251671
http://dx.doi.org/10.1371/journal.pone.0052002