Melanocytes—A Novel Tool to Study Mitochondrial Dysfunction in Duchenne Muscular Dystrophy

Dystrophin is a subsarcolemmal protein that, by linking the actin cytoskeleton to the extracellular matrix via dystroglycans, is critical for the integrity of muscle fibers. Here, we report that epidermal melanocytes, obtained from conventional skin biopsy, express dystrophin with a restricted local...

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Detalles Bibliográficos
Autores principales: Pellegrini, Camilla, Zulian, Alessandra, Gualandi, Francesca, Manzati, Elisa, Merlini, Luciano, Michelini, Maria E, Benassi, Luisa, Marmiroli, Sandra, Ferlini, Alessandra, Sabatelli, Patrizia, Bernardi, Paolo, Maraldi, Nadir M
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wiley Subscription Services, Inc., A Wiley Company 2013
Materias:
Original Research Articles
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3601437/
https://www.ncbi.nlm.nih.gov/pubmed/23169061
http://dx.doi.org/10.1002/jcp.24290

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3601437/
https://www.ncbi.nlm.nih.gov/pubmed/23169061
http://dx.doi.org/10.1002/jcp.24290

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