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Congenital Hyperinsulinism Caused by Hexokinase I Expression or Glucokinase-Activating Mutation in a Subset of β-Cells

Congenital hyperinsulinism causes persistent hypoglycemia in neonates and infants. Most often, uncontrolled insulin secretion (IS) results from a lack of functional K(ATP) channels in all β-cells or only in β-cells within a resectable focal lesion. In more rare cases, without K(ATP) channel mutation...

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Detalles Bibliográficos
Autores principales: Henquin, Jean-Claude, Sempoux, Christine, Marchandise, Joelle, Godecharles, Sebastien, Guiot, Yves, Nenquin, Myriam, Rahier, Jacques
Formato: Online Artículo Texto
Lenguaje:English
Publicado: American Diabetes Association 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3636634/
https://www.ncbi.nlm.nih.gov/pubmed/23274908
http://dx.doi.org/10.2337/db12-1414