Omigapil Treatment Decreases Fibrosis and Improves Respiratory Rate in dy(2J) Mouse Model of Congenital Muscular Dystrophy

INTRODUCTION: Congenital muscular dystrophy is a distinct group of diseases presenting with weakness in infancy or childhood and no current therapy. One form, MDC1A, is the result of laminin alpha-2 deficiency and results in significant weakness, respiratory insufficiency and early death. Modificati...

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Detalles Bibliográficos
Autores principales: Yu, Qing, Sali, Arpana, Van der Meulen, Jack, Creeden, Brittany K., Gordish-Dressman, Heather, Rutkowski, Anne, Rayavarapu, Sree, Uaesoontrachoon, Kitipong, Huynh, Tony, Nagaraju, Kanneboyina, Spurney, Christopher F.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2013
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3675144/
https://www.ncbi.nlm.nih.gov/pubmed/23762378
http://dx.doi.org/10.1371/journal.pone.0065468

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3675144/
https://www.ncbi.nlm.nih.gov/pubmed/23762378
http://dx.doi.org/10.1371/journal.pone.0065468

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