N-Acetyl-L-Cysteine Prevents Stress-Induced Desmin Aggregation in Cellular Models of Desminopathy

Mutations within the human desmin gene are responsible for a subcategory of myofibrillar myopathies called desminopathies. However, a single inherited mutation can produce different phenotypes within a family, suggesting that environmental factors influence disease states. Although several mouse mod...

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Detalles Bibliográficos
Autores principales: Segard, Bertrand-David, Delort, Florence, Bailleux, Virginie, Simon, Stéphanie, Leccia, Emilie, Gausseres, Blandine, Briki, Fatma, Vicart, Patrick, Batonnet-Pichon, Sabrina
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2013
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3788106/
https://www.ncbi.nlm.nih.gov/pubmed/24098483
http://dx.doi.org/10.1371/journal.pone.0076361

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3788106/
https://www.ncbi.nlm.nih.gov/pubmed/24098483
http://dx.doi.org/10.1371/journal.pone.0076361

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