Progressive Retinal Degeneration and Glial Activation in the CLN6(nclf) Mouse Model of Neuronal Ceroid Lipofuscinosis: A Beneficial Effect of DHA and Curcumin Supplementation

Neuronal ceroid lipofuscinosis (NCL) is a group of neurodegenerative lysosomal storage disorders characterized by vision loss, mental and motor deficits, and spontaneous seizures. Neuropathological analyses of autopsy material from NCL patients and animal models revealed brain atrophy closely associ...

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Detalles Bibliográficos
Autores principales: Mirza, Myriam, Volz, Cornelia, Karlstetter, Marcus, Langiu, Monica, Somogyi, Aleksandra, Ruonala, Mika O., Tamm, Ernst R., Jägle, Herbert, Langmann, Thomas
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2013
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3790850/
https://www.ncbi.nlm.nih.gov/pubmed/24124525
http://dx.doi.org/10.1371/journal.pone.0075963

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3790850/
https://www.ncbi.nlm.nih.gov/pubmed/24124525
http://dx.doi.org/10.1371/journal.pone.0075963

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