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Specific cancer rates may differ in patients with hereditary haemorrhagic telangiectasia compared to controls

BACKGROUND: Hereditary haemorrhagic telangiectasia (HHT) is inherited as an autosomal dominant trait, affects ~1 in 5,000, and causes multi-systemic vascular lesions and life-limiting complications. Life expectancy is surprisingly good, particularly for patients over 60ys. We hypothesised that indiv...

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Detalles Bibliográficos
Autores principales: Hosman, Anna E, Devlin, Hannah L, Silva, B Maneesha, Shovlin, Claire L
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3891994/
https://www.ncbi.nlm.nih.gov/pubmed/24354965
http://dx.doi.org/10.1186/1750-1172-8-195