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Generalized Lichen Nitidus in a boy with Niemann-Pick disease type B

Generalized lichen nitidus is an uncommon chronic inflammatory dermatosis with very characteristic histological findings. Its pathogenesis is still unclear; very rarely it has been associated with genetic disorders. Herein we report the case of a 12-year-old boy with Niemann-Pick disease who develop...

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Detalles Bibliográficos
Autores principales: Teixeira, Vera Barreto, Coutinho, Inês, Cardoso, José Carlos, Tellhechea, Óscar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2013
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3900352/
https://www.ncbi.nlm.nih.gov/pubmed/24474110
http://dx.doi.org/10.1590/abd1806-4841.20132829