Cargando…

Notch signaling deficiency underlies age-dependent depletion of satellite cells in muscular dystrophy

Duchenne muscular dystrophy (DMD) is a devastating disease characterized by muscle wasting, loss of mobility and death in early adulthood. Satellite cells are muscle-resident stem cells responsible for the repair and regeneration of damaged muscles. One pathological feature of DMD is the progressive...

Descripción completa

Detalles Bibliográficos
Autores principales:	Jiang, Chunhui, Wen, Yefei, Kuroda, Kazuki, Hannon, Kevin, Rudnicki, Michael A., Kuang, Shihuan
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Limited 2014
Materias:	Research Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4107328/ https://www.ncbi.nlm.nih.gov/pubmed/24906372 http://dx.doi.org/10.1242/dmm.015917

Ejemplares similares

Satellite cell contribution to disease pathology in Duchenne muscular dystrophy
por: Kodippili, Kasun, et al.
Publicado: (2023)

Depletion of skeletal muscle satellite cells attenuates pathology in muscular dystrophy
por: Boyer, Justin G., et al.
Publicado: (2022)

A POGLUT1 mutation causes a muscular dystrophy with reduced Notch signaling and satellite cell loss
por: Servián‐Morilla, Emilia, et al.
Publicado: (2016)

Implications of notch signaling in duchenne muscular dystrophy
por: Den Hartog, Lily, et al.
Publicado: (2022)

Canonical Wnt signaling induces BMP-4 to specify slow myofibrogenesis of fetal myoblasts
por: Kuroda, Kazuki, et al.
Publicado: (2013)

Satellite Cells: Regenerative Mechanisms and Applicability in Muscular Dystrophy
por: de Souza, Gustavo Torres, et al.
Publicado: (2015)

Megf10 regulates the progression of the satellite cell myogenic program
por: Holterman, Chet E., et al.
Publicado: (2007)

Defining and identifying satellite cell-opathies within muscular dystrophies and myopathies
por: Ganassi, Massimo, et al.
Publicado: (2022)

PPARδ regulates satellite cell proliferation and skeletal muscle regeneration
por: Angione, Alison R, et al.
Publicado: (2011)

Stage-specific effects of Notch activation during skeletal myogenesis
por: Bi, Pengpeng, et al.
Publicado: (2016)

Progressive Muscular Dystrophy in α-Sarcoglycan–deficient Mice
por: Duclos, Franck, et al.
Publicado: (1998)

ANT-dependent MPTP underlies necrotic myofiber death in muscular dystrophy
por: Bround, Michael J., et al.
Publicado: (2023)

Targeting muscle stem cell intrinsic defects to treat Duchenne muscular dystrophy
por: Dumont, Nicolas A, et al.
Publicado: (2016)

Cellular and molecular mechanisms underlying muscular dystrophy
por: Rahimov, Fedik, et al.
Publicado: (2013)

Nuclear entrapment and extracellular depletion of PCOLCE is associated with muscle degeneration in oculopharyngeal muscular dystrophy
por: Raz, Vered, et al.
Publicado: (2013)

Muscle satellite cells and impaired late stage regeneration in different murine models for muscular dystrophies
por: Ribeiro, Antonio F., et al.
Publicado: (2019)

Molecular Signatures of Membrane Protein Complexes Underlying Muscular Dystrophy
por: Turk, Rolf, et al.
Publicado: (2016)

uPA deficiency exacerbates muscular dystrophy in MDX mice
por: Suelves, Mònica, et al.
Publicado: (2007)

uPA deficiency exacerbates muscular dystrophy in MDX mice
por: Suelves, Mònica, et al.
Publicado: (2007)

New aspects on patients affected by dysferlin deficient muscular dystrophy
por: Klinge, Lars, et al.
Publicado: (2009)

Effects of rituximab in two patients with dysferlin-deficient muscular dystrophy
por: Lerario, Alberto, et al.
Publicado: (2010)

Glycogenin-1 deficiency mimicking limb-girdle muscular dystrophy
por: Lefeuvre, Claire, et al.
Publicado: (2020)

Anesthetic Care of a Child With Merosin-Deficient Muscular Dystrophy
por: Munlemvo, Dolly M., et al.
Publicado: (2020)

MSTO1 mutations cause mtDNA depletion, manifesting as muscular dystrophy with cerebellar involvement
por: Donkervoort, S., et al.
Publicado: (2019)

High-Content Screening of Human Primary Muscle Satellite Cells for New Therapies for Muscular Atrophy/Dystrophy
por: Nierobisz, Lidia S, et al.
Publicado: (2013)

Myopathologic trajectory in Duchenne muscular dystrophy (DMD) reveals lack of regeneration due to senescence in satellite cells
por: Cardone, Nastasia, et al.
Publicado: (2023)

Saying NO to muscular dystrophy
por: Dove, Alan W.
Publicado: (2001)

Fatigue in muscular dystrophies
por: Angelini, Corrado, et al.
Publicado: (2012)

δ-Sarcoglycan-deficient muscular dystrophy: from discovery to therapeutic approaches
por: Blain, Alison M, et al.
Publicado: (2011)

Respiratory and cardiac function in congenital muscular dystrophies with alpha dystroglycan deficiency
por: Pane, M., et al.
Publicado: (2012)

Dystrophin-deficient muscular dystrophy in a Toy Poodle with a single base pair insertion in exon 45 of the Duchenne muscular dystrophy gene
por: SAKAI, Kosei, et al.
Publicado: (2022)

Angiogenesis as a novel therapeutic strategy for Duchenne muscular dystrophy through decreased ischemia and increased satellite cells
por: Shimizu-Motohashi, Yuko, et al.
Publicado: (2014)

Derivation and Characterization of Immortalized Human Muscle Satellite Cell Clones from Muscular Dystrophy Patients and Healthy Individuals
por: Massenet, Jimmy, et al.
Publicado: (2020)

Cardiac Dysrhythmias, Cardiomyopathy and Muscular Dystrophy in Patients with Emery-Dreifuss Muscular Dystrophy and Limb-Girdle Muscular Dystrophy Type 1B
por: Hong, Jong-Seo, et al.
Publicado: (2005)

Antioxidants Reduce Muscular Dystrophy in the dy(2J)/dy(2J) Mouse Model of Laminin α2 Chain-Deficient Muscular Dystrophy
por: Harandi, Vahid M., et al.
Publicado: (2020)

Longitudinal Study of Three microRNAs in Duchenne Muscular Dystrophy and Becker Muscular Dystrophy
por: Trifunov, Selena, et al.
Publicado: (2020)

Genetic Patterns of Selected Muscular Dystrophies in the Muscular Dystrophy Surveillance, Tracking, and Research Network
por: Kang, Peter B., et al.
Publicado: (2023)

Characteristics of Japanese Patients with Becker Muscular Dystrophy and Intermediate Muscular Dystrophy in a Japanese National Registry of Muscular Dystrophy (Remudy): Heterogeneity and Clinical Variation
por: Mori-Yoshimura, Madoka, et al.
Publicado: (2018)

Comparative proteomic analyses of Duchenne muscular dystrophy and Becker muscular dystrophy muscles: changes contributing to preserve muscle function in Becker muscular dystrophy patients
por: Capitanio, Daniele, et al.
Publicado: (2020)

Attenuated muscle regeneration is a key factor in dysferlin-deficient muscular dystrophy
por: Chiu, Yen-Hui, et al.
Publicado: (2009)

Cannot write session to /tmp/vufind_sessions/sess_dlv02jif2thm1ns3hnjlbtfahg