Differentiation defects in primary motoneurons from a SMARD1 mouse model that are insensitive to treatment with low dose PEGylated IGF1

Muscle atrophy and diaphragmatic palsy are the clinical characteristics of spinal muscular atrophy with respiratory distress type 1 (SMARD1), and are well represented in the neuromuscular degeneration (Nmd(2J)) mouse, modeling the juvenile form of SMARD1. Both in humans and mice mutations in the IGH...

Descripción completa

Detalles Bibliográficos
Autores principales: Krieger, Frank, Metzger, Friedrich, Jablonka, Sibylle
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Landes Bioscience 2014
Materias:
Addendum
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4116388/
https://www.ncbi.nlm.nih.gov/pubmed/25083343
http://dx.doi.org/10.4161/rdis.29415

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4116388/
https://www.ncbi.nlm.nih.gov/pubmed/25083343
http://dx.doi.org/10.4161/rdis.29415

Ejemplares similares