Cargando…
Functional Changes in Pulmonary Arterial Endothelial Cells Associated with BMPR2 Mutations
Pulmonary arterial hypertension (PAH) is a devastating disease characterized by abnormal remodeling of small, peripheral pulmonary arteries. Germline mutations in the bone morphogenetic protein receptor type 2 (BMPR2) gene are a major risk factor for developing PAH. At present, the correlation betwe...
Autores principales: | , , , , , , , , , , , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2014
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4154762/ https://www.ncbi.nlm.nih.gov/pubmed/25187962 http://dx.doi.org/10.1371/journal.pone.0106703 |