Cyclosporin A Promotes in vivo Myogenic Response in Collagen VI-Deficient Myopathic Mice

Mutations of genes encoding for collagen VI cause various muscle diseases in humans, including Bethlem myopathy and Ullrich congenital muscular dystrophy. Collagen VI null (Col6a1(−/−)) mice are affected by a myopathic phenotype with mitochondrial dysfunction, spontaneous apoptosis of muscle fibers,...

Descripción completa

Detalles Bibliográficos
Autores principales: Gattazzo, Francesca, Molon, Sibilla, Morbidoni, Valeria, Braghetta, Paola, Blaauw, Bert, Urciuolo, Anna, Bonaldo, Paolo
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2014
Materias:
Neuroscience
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4163991/
https://www.ncbi.nlm.nih.gov/pubmed/25309428
http://dx.doi.org/10.3389/fnagi.2014.00244

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4163991/
https://www.ncbi.nlm.nih.gov/pubmed/25309428
http://dx.doi.org/10.3389/fnagi.2014.00244

Ejemplares similares