A case of congenital TTP presenting with microganiopathy in adulthood

BACKGROUND: Congenital thrombotic thrombocytopenic purpura (TTP), also known as Upshaw-Schulman Syndrome is a rare inherited deficiency of ADAMTS13. Unlike the more common acquired TTP which is characterized by an acquired inhibitor of ADAMTS13, patients with congenital TTP have an absolute deficien...

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Detalles Bibliográficos
Autores principales: Gallivan, Chris D, Conrad, David M, Kew, Andrea K
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2014
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4168056/
https://www.ncbi.nlm.nih.gov/pubmed/25243071
http://dx.doi.org/10.1186/2052-1839-14-16

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4168056/
https://www.ncbi.nlm.nih.gov/pubmed/25243071
http://dx.doi.org/10.1186/2052-1839-14-16

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