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A Girl with Autoimmune Cytopenias, Nonmalignant Lymphadenopathy, and Recurrent Infections

We describe a girl, now 9 years of age, with chronic idiopathic thrombocytopenic purpura, persistent nonmalignant lymphadenopathy, splenomegaly, recurrent infections, and autoimmune hemolytic anemia. Her symptoms partly fit the definitions of both autoimmune lymphoproliferative syndrome (ALPS) and c...

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Detalles Bibliográficos
Autores principales: Mattheij, Marjolein A. C., Schatorjé, Ellen J. H., Gemen, Eugenie F. A., van de Corput, Lisette, Nooijen, Peet T. G. A., van der Burg, Mirjam, de Vries, Esther
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi Publishing Corporation 2012
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4207596/
https://www.ncbi.nlm.nih.gov/pubmed/25379303
http://dx.doi.org/10.1155/2012/196417