4-Phenylbutyrate Attenuates the ER Stress Response and Cyclic AMP Accumulation in DYT1 Dystonia Cell Models

Dystonia is a neurological disorder in which sustained muscle contractions induce twisting and repetitive movements or abnormal posturing. DYT1 early-onset primary dystonia is the most common form of hereditary dystonia and is caused by deletion of a glutamic acid residue (302/303) near the carboxyl...

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Detalles Bibliográficos
Autores principales: Cho, Jin A., Zhang, Xuan, Miller, Gregory M., Lencer, Wayne I., Nery, Flavia C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2014
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4224384/
https://www.ncbi.nlm.nih.gov/pubmed/25379658
http://dx.doi.org/10.1371/journal.pone.0110086

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4224384/
https://www.ncbi.nlm.nih.gov/pubmed/25379658
http://dx.doi.org/10.1371/journal.pone.0110086

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