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4-Phenylbutyrate Attenuates the ER Stress Response and Cyclic AMP Accumulation in DYT1 Dystonia Cell Models
Dystonia is a neurological disorder in which sustained muscle contractions induce twisting and repetitive movements or abnormal posturing. DYT1 early-onset primary dystonia is the most common form of hereditary dystonia and is caused by deletion of a glutamic acid residue (302/303) near the carboxyl...
Autores principales: | Cho, Jin A., Zhang, Xuan, Miller, Gregory M., Lencer, Wayne I., Nery, Flavia C. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2014
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4224384/ https://www.ncbi.nlm.nih.gov/pubmed/25379658 http://dx.doi.org/10.1371/journal.pone.0110086 |
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