Cargando…

The neural crest lineage as a driver of disease heterogeneity in Tuberous Sclerosis Complex and Lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a rare neoplastic disease, best characterized by the formation of proliferative nodules that express smooth muscle and melanocytic antigens within the lung parenchyma, leading to progressive destruction of lung tissue and function. The pathological basis of LAM is a...

Descripción completa

Detalles Bibliográficos
Autores principales: Delaney, Sean P., Julian, Lisa M., Stanford, William L.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2014
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4243694/
https://www.ncbi.nlm.nih.gov/pubmed/25505789
http://dx.doi.org/10.3389/fcell.2014.00069