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Systemic Amyloidosis: Lessons from β(2)-Microglobulin

β(2)-Microglobulin is responsible for systemic amyloidosis affecting patients undergoing long-term hemodialysis. Its genetic variant D76N causes a very rare form of familial systemic amyloidosis. These two types of amyloidoses differ significantly in terms of the tissue localization of deposits and...

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Detalles Bibliográficos
Autores principales: Stoppini, Monica, Bellotti, Vittorio
Formato: Online Artículo Texto
Lenguaje:English
Publicado: American Society for Biochemistry and Molecular Biology 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4400370/
https://www.ncbi.nlm.nih.gov/pubmed/25750126
http://dx.doi.org/10.1074/jbc.R115.639799