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Fulminant primary manifestations of Wegener’s granulomatosis might not be pauci-immune

Wegener’s granulomatosis is an ANCA-associated small vessel vasculitis. Because histologically immune complex deposits are frequently lacking, the term pauci-immune has been introduced for this subgroup. We report a patient with fulminant, severe PR3-ANCA-positive Wegener’s granulomatosis and multi-...

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Detalles Bibliográficos
Autores principales: Schönermarck, Ulf, Grahovac, Maja, Sárdy, Miklós, Dolch, Michael, Wollenberg, Andreas
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2010
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421412/
https://www.ncbi.nlm.nih.gov/pubmed/25949469
http://dx.doi.org/10.1093/ndtplus/sfq145