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Fulminant primary manifestations of Wegener’s granulomatosis might not be pauci-immune
Wegener’s granulomatosis is an ANCA-associated small vessel vasculitis. Because histologically immune complex deposits are frequently lacking, the term pauci-immune has been introduced for this subgroup. We report a patient with fulminant, severe PR3-ANCA-positive Wegener’s granulomatosis and multi-...
Autores principales: | Schönermarck, Ulf, Grahovac, Maja, Sárdy, Miklós, Dolch, Michael, Wollenberg, Andreas |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2010
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4421412/ https://www.ncbi.nlm.nih.gov/pubmed/25949469 http://dx.doi.org/10.1093/ndtplus/sfq145 |
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