Wild Type Mesenchymal Cells Contribute to the Lung Pathology of Lymphangioleiomyomatosis

Lymphangioleiomyomatosis (LAM) is a rare disease leading to lungs cysts and progressive respiratory failure. Cells of unknown origin accumulate in the lungs forming nodules and eventually resulting in lung cysts. These LAM cells are described as clonal with bi-allelic mutations in TSC-2 resulting in...

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Detalles Bibliográficos
Autores principales: Clements, Debbie, Dongre, Arundhati, Krymskaya, Vera P., Johnson, Simon R.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2015
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4433241/
https://www.ncbi.nlm.nih.gov/pubmed/25978616
http://dx.doi.org/10.1371/journal.pone.0126025

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4433241/
https://www.ncbi.nlm.nih.gov/pubmed/25978616
http://dx.doi.org/10.1371/journal.pone.0126025

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