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Wild Type Mesenchymal Cells Contribute to the Lung Pathology of Lymphangioleiomyomatosis
Lymphangioleiomyomatosis (LAM) is a rare disease leading to lungs cysts and progressive respiratory failure. Cells of unknown origin accumulate in the lungs forming nodules and eventually resulting in lung cysts. These LAM cells are described as clonal with bi-allelic mutations in TSC-2 resulting in...
| Autores principales: | , , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
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Public Library of Science
2015
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4433241/ https://www.ncbi.nlm.nih.gov/pubmed/25978616 http://dx.doi.org/10.1371/journal.pone.0126025 |