Diffuse left ventricular interstitial fibrosis is associated with sub-clinical myocardial dysfunction in Alström Syndrome: an observational study

BACKGROUND: Alström syndrome is a rare inherited ciliopathy with progressive multisystem involvement. Dilated cardiomyopathy is common in infancy and recurs or presents de novo in adults with high rates of premature cardiovascular death. Although Alström syndrome is characterised by fibrosis in soli...

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Detalles Bibliográficos
Autores principales: Edwards, Nicola C., Moody, William E., Yuan, Mengshi, Warfield, Adrian T., Cramb, Robert, Paisey, Richard B., Geberhiwot, Tarekegn, Steeds, Richard P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2015
Materias:
Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4483224/
https://www.ncbi.nlm.nih.gov/pubmed/26104972
http://dx.doi.org/10.1186/s13023-015-0292-z

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4483224/
https://www.ncbi.nlm.nih.gov/pubmed/26104972
http://dx.doi.org/10.1186/s13023-015-0292-z

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