A new cellular model to follow Friedreich's ataxia development in a time-resolved way

Friedreich's ataxia (FRDA) is a recessive autosomal ataxia caused by reduced levels of frataxin (FXN), an essential mitochondrial protein that is highly conserved from bacteria to primates. The exact role of frataxin and its primary function remain unclear although this information would be ver...

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Detalles Bibliográficos
Autores principales: Vannocci, Tommaso, Faggianelli, Nathalie, Zaccagnino, Silvia, della Rosa, Ilaria, Adinolfi, Salvatore, Pastore, Annalisa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Company of Biologists 2015
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4486863/
https://www.ncbi.nlm.nih.gov/pubmed/26035392
http://dx.doi.org/10.1242/dmm.020545

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4486863/
https://www.ncbi.nlm.nih.gov/pubmed/26035392
http://dx.doi.org/10.1242/dmm.020545

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