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Familial Hemophagocytic Lymphohistiocytosis Presenting as Hydrops Fetalis

Background Familial hemophagocytic lymphohistiocytosis (FLH) is an autosomal recessive disorder of immune regulation that leads to a hyperinflammatory syndrome. Fetal onset FHL is extremely rare and is considered to be the most severe form of FHL. Case We report a preterm case of FHL that presented...

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Detalles Bibliográficos
Autores principales: Iwatani, Sota, Uemura, Kazuya, Mizobuchi, Masami, Yoshimoto, Seiji, Kawasaki, Keiichiro, Kosaka, Yoshiyuki, Hori, Masayuki, Yasumi, Takahiro, Nakao, Hideto
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Thieme Medical Publishers 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4502624/
https://www.ncbi.nlm.nih.gov/pubmed/26199792
http://dx.doi.org/10.1055/s-0034-1544110