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Measuring Neuromuscular Junction Functionality in the SOD1(G93A) Animal Model of Amyotrophic Lateral Sclerosis

Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease that leads to motor neuron degeneration, alteration in neuromuscular junctions (NMJs), muscle atrophy, and paralysis. To investigate the NMJ functionality in ALS we tested, in vitro, two innervated muscle types excised from SOD...

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Detalles Bibliográficos
Autores principales: Rizzuto, Emanuele, Pisu, Simona, Musarò, Antonio, Del Prete, Zaccaria
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer US 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4516896/
https://www.ncbi.nlm.nih.gov/pubmed/25631208
http://dx.doi.org/10.1007/s10439-015-1259-x