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Impaired cardiac and peripheral hemodynamic responses to inhaled β(2)-agonist in cystic fibrosis

BACKGROUND: Pulmonary system dysfunction is a hallmark of cystic fibrosis (CF) disease. In addition to impaired cystic fibrosis transmembrane conductance regulator protein, dysfunctional β(2)-adrenergic receptors (β(2)AR) contribute to low airway function in CF. Recent observations suggest CF may al...

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Detalles Bibliográficos
Autores principales: Van Iterson, Erik H., Karpen, Stephen R., Baker, Sarah E., Wheatley, Courtney M., Morgan, Wayne J., Snyder, Eric M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4560914/
https://www.ncbi.nlm.nih.gov/pubmed/26341519
http://dx.doi.org/10.1186/s12931-015-0270-y