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Dysferlinopathy Fibroblasts Are Defective in Plasma Membrane Repair

Background: Dysferlin is a sarcolemmal protein that is defective in Miyoshi myopathy and limb-girdle muscular dystrophy type 2B, and is involved in sarcolemmal repair. Primary cultured myoblasts and myotubes established from patient muscle biopsies have been widely utilized to explore the molecular...

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Detalles Bibliográficos
Autores principales: Matsuda, Chie, Kiyosue, Kazuyuki, Nishino, Ichizo, Goto, Yuichi, Hayashi, Yukiko K.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2015
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4639325/
https://www.ncbi.nlm.nih.gov/pubmed/26579332
http://dx.doi.org/10.1371/currents.md.5865add2d766f39a0e0411d38a7ba09c