Cargando…
Dysferlinopathy Fibroblasts Are Defective in Plasma Membrane Repair
Background: Dysferlin is a sarcolemmal protein that is defective in Miyoshi myopathy and limb-girdle muscular dystrophy type 2B, and is involved in sarcolemmal repair. Primary cultured myoblasts and myotubes established from patient muscle biopsies have been widely utilized to explore the molecular...
Autores principales: | Matsuda, Chie, Kiyosue, Kazuyuki, Nishino, Ichizo, Goto, Yuichi, Hayashi, Yukiko K. |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Public Library of Science
2015
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4639325/ https://www.ncbi.nlm.nih.gov/pubmed/26579332 http://dx.doi.org/10.1371/currents.md.5865add2d766f39a0e0411d38a7ba09c |
Ejemplares similares
-
Muscle membrane repair and inflammatory attack in dysferlinopathy
por: Han, Renzhi
Publicado: (2011) -
AMPK Complex Activation Promotes Sarcolemmal Repair in Dysferlinopathy
por: Ono, Hiroya, et al.
Publicado: (2020) -
Therapeutic exon skipping for dysferlinopathies?
por: Aartsma-Rus, Annemieke, et al.
Publicado: (2010) -
Lack of Correlation between Outcomes of Membrane Repair Assay and Correction of Dystrophic Changes in Experimental Therapeutic Strategy in Dysferlinopathy
por: Lostal, William, et al.
Publicado: (2012) -
Dysferlin and Animal Models for Dysferlinopathy
por: Kobayashi, Kinji, et al.
Publicado: (2012)