Peutz-Jeghers Syndrome With Diffuse Gastrointestinal Polyposis: Three Cases in a Family With Different Manifestations and No Evidence of Malignancy During 14 Years Follow Up

INTRODUCTION: Peutz-Jeghers syndrome (PJS) is a rare disorder characterized by mucocutaneous perioral pigmentation, gastrointestinal hamartomatous polyposis, and an increased risk of malignancy. Families with PJS may show a variable spectrum of manifestations in spite of their consecutive generation...

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Detalles Bibliográficos
Autores principales: Matini, Esfandiar, Houshangi, Hooman, Jangholi, Ehsan, Farjad Azad, Pantea, Najibpour, Reza, Farshad, Ali
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Kowsar 2015
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4706732/
https://www.ncbi.nlm.nih.gov/pubmed/26756003
http://dx.doi.org/10.5812/ircmj.19271

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4706732/
https://www.ncbi.nlm.nih.gov/pubmed/26756003
http://dx.doi.org/10.5812/ircmj.19271

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