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Radical nephrectomy and regional lymph node dissection for locally advanced type 2 papillary renal cell carcinoma in an at-risk individual from a family with hereditary leiomyomatosis and renal cell cancer: a case report

BACKGROUND: Hereditary leiomyomatosis and renal cell carcinoma (HLRCC) is an autosomal dominant tumor susceptibility syndrome, and the disease-related gene has been identified as fumarate hydratase (fumarase, FH). HLRCC-associated kidney cancer is an aggressive tumor characterized by early metastasi...

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Detalles Bibliográficos
Autores principales: Kamai, Takao, Abe, Hideyuki, Arai, Kyoko, Murakami, Satoshi, Sakamoto, Setsu, Kaji, Yasushi, Yoshida, Ken-Ichiro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4794818/
https://www.ncbi.nlm.nih.gov/pubmed/26983443
http://dx.doi.org/10.1186/s12885-016-2272-7