Abnormal proplatelet formation and emperipolesis in cultured human megakaryocytes from gray platelet syndrome patients

The Gray Platelet Syndrome (GPS) is a rare inherited bleeding disorder characterized by deficiency of platelet α-granules, macrothrombocytopenia and marrow fibrosis. The autosomal recessive form of GPS is linked to loss of function mutations in NBEAL2, which is predicted to regulate granule traffick...

Descripción completa

Detalles Bibliográficos
Autores principales: Di Buduo, Christian A., Alberelli, Maria Adele, Glembostky, Ana C., Podda, Gianmarco, Lev, Paola R., Cattaneo, Marco, Landolfi, Raffaele, Heller, Paula G., Balduini, Alessandra, De Candia, Erica
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Nature Publishing Group 2016
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4796794/
https://www.ncbi.nlm.nih.gov/pubmed/26987485
http://dx.doi.org/10.1038/srep23213

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4796794/
https://www.ncbi.nlm.nih.gov/pubmed/26987485
http://dx.doi.org/10.1038/srep23213

Ejemplares similares