Early Impairment of Lung Mechanics in a Murine Model of Marfan Syndrome

Early morbidity and mortality in patients with Marfan syndrome (MFS) -a connective tissue disease caused by mutations in fibrillin-1 gene- are mainly caused by aorta aneurysm and rupture. However, the increase in the life expectancy of MFS patients recently achieved by reparatory surgery promotes cl...

Descripción completa

Detalles Bibliográficos
Autores principales: Uriarte, Juan J., Meirelles, Thayna, Gorbenko del Blanco, Darya, Nonaka, Paula N., Campillo, Noelia, Sarri, Elisabet, Navajas, Daniel, Egea, Gustavo, Farré, Ramon
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2016
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4803219/
https://www.ncbi.nlm.nih.gov/pubmed/27003297
http://dx.doi.org/10.1371/journal.pone.0152124

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4803219/
https://www.ncbi.nlm.nih.gov/pubmed/27003297
http://dx.doi.org/10.1371/journal.pone.0152124

Ejemplares similares