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Effects of Pin1 Loss in Hdh(Q111) Knock-in Mice

Huntington’s disease (HD) is a fatal, dominantly inherited, neurodegenerative disorder due to a pathological expansion of the CAG repeat in the coding region of the HTT gene. In the quest for understanding the molecular basis of neurodegeneration, we have previously demonstrated that the prolyl isom...

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Detalles Bibliográficos
Autores principales: Agostoni, Elena, Michelazzi, Silvia, Maurutto, Marta, Carnemolla, Alisia, Ciani, Yari, Vatta, Paolo, Roncaglia, Paola, Zucchelli, Silvia, Leanza, Giampiero, Mantovani, Fiamma, Gustincich, Stefano, Santoro, Claudio, Piazza, Silvano, Del Sal, Giannino, Persichetti, Francesca
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4852193/
https://www.ncbi.nlm.nih.gov/pubmed/27199664
http://dx.doi.org/10.3389/fncel.2016.00110