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Reduced Right Ventricular Native Myocardial T(1) in Anderson-Fabry Disease: Comparison to Pulmonary Hypertension and Healthy Controls

AIMS: Anderson-Fabry disease (AFD) is characterized by progressive multiorgan accumulation of intracellular sphingolipids due to α-galactosidase A enzyme deficiency, resulting in progressive ventricular hypertrophy, heart failure, arrhythmias, and death. Decreased native (non-contrast) left ventricu...

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Detalles Bibliográficos
Autores principales: Pagano, Joseph J., Chow, Kelvin, Khan, Aneal, Michelakis, Evangelos, Paterson, Ian, Oudit, Gavin Y., Thompson, Richard B.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2016
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4909219/
https://www.ncbi.nlm.nih.gov/pubmed/27305064
http://dx.doi.org/10.1371/journal.pone.0157565